Vulvar dermatofibrosarcoma of Darier and Ferrand in a young woman: About a new observation

Darier and Ferrand Dermatofibrosarcoma is a rare mesenchymal tumor in young adults, often located in the trunk. We report an observation of a vulvar localization of dermatofibrosarcoma Darier and Ferrand. It was a young patient, aged 25, who presented a tumor of the vulvar region. This tumor has been evolving for about 10 years in two phases, the first of which is longer, with very slow development, and a second phase characterized by rapid growth of the tumor coinciding with the start of pregnancy. The examination noted a tumor developed at the expense of the vulvar region. The diagnosis of dermatofibrosarcoma was retained in view of a characteristic histopathological appearance. The treatment consisted of resection surgery with margins of about 5 cm followed by reconstruction by direct suture. The evolution, in the immediate aftermath, was good. Vulvar localization of dermatofibrosarcoma is possible. Key words: Darier and Ferrand dermatofibrosarcoma, Vulva, Young woman