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Thoracoabdominal aortic replacement in a 6-year-old boy with Loeys-Dietz syndrome
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Abstract
Connective tissue disorders such as Marfan- and Loeys-Dietz syndrome (LDS) can lead to aortic aneurysms and aortic dissections in children. Patients with LDS often necessitating multiple aortic surgeries throughout their lives to extend their lifespan. A boy underwent Bentall procedure at the age of three for aortic aneurysm. On August 4, 2023, this boy was referred to the hospital again due to severe abdominal pain. CTA indicates aortic dissection (DeBakey Type III, Stanford Type B). After a multidisciplinary team discussion, a successful thoracoabdominal aortic replacement was performed.
Title: Thoracoabdominal aortic replacement in a 6-year-old boy with Loeys-Dietz syndrome
Description:
Abstract
Connective tissue disorders such as Marfan- and Loeys-Dietz syndrome (LDS) can lead to aortic aneurysms and aortic dissections in children.
Patients with LDS often necessitating multiple aortic surgeries throughout their lives to extend their lifespan.
A boy underwent Bentall procedure at the age of three for aortic aneurysm.
On August 4, 2023, this boy was referred to the hospital again due to severe abdominal pain.
CTA indicates aortic dissection (DeBakey Type III, Stanford Type B).
After a multidisciplinary team discussion, a successful thoracoabdominal aortic replacement was performed.
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