Large Fibroid arising from Mullerian Remnant Mimicking as Ovarian Neoplasm in a Woman with MRKH Syndrome

ABSTRACTIn this article, a large leiomyoma with degenerative changes arising from the rudimentary uterine knob in a patient with Mayer- Rokitansky-Kuster-Hauser (MRKH) syndrome and mimicking an ovarian neoplasm is reported.The patient was a 39-year-old woman, known case of MRKH with vaginal aplasia who presented with pain abdomen, loss of appetite and weight. On physical examination, a large pelvic mass was detected. A provisional diagnosis of left ovarian neoplasm was made on USG and CT scan for which an exploratory laparotomy was performed. Finally, it was diagnosed as a case of multiple leiomyomas with hyaline degeneration on histopathological examination.Myoma arising from a rudimentary uterine knob/anlage is a rare finding but should be considered in the differential diagnosis of pelvic mass in patients with MRKH syndrome.How to cite this articleSingh S, Chakravarty B, Chakravarty M, Chakravarty A. Large Fibroid arising from Mullerian Remnant Mimicking as Ovarian Neoplasm in a Woman with MRKH Syndrome. Int J Infertility Fetal Med 2012;3(1):30-32.