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Hypohidrotic ectodermal dysplasia and finger clubbing – An unknown association
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The ectodermal dysplasias are heterogenous group of inherited disorders with primary defects in tissues derived from embryonic ectoderm such as hair, tooth, nail and sweat gland. This disorder is broadly divided into hypohidrotic or anhidrotic and hidrotic forms. Here, we present a classical x-linked hypohidrotic ectodermal dysplasia with finger clubbing, the association of which is not being reported earlier.
DOI: http://dx.doi.org/10.3126/ajms.v5i4.9457
Asian Journal of Medical Sciences 2014 Vol.5(4); 119-121
Pharmamedix India Publication Pvt Ltd
Title: Hypohidrotic ectodermal dysplasia and finger clubbing – An unknown association
Description:
The ectodermal dysplasias are heterogenous group of inherited disorders with primary defects in tissues derived from embryonic ectoderm such as hair, tooth, nail and sweat gland.
This disorder is broadly divided into hypohidrotic or anhidrotic and hidrotic forms.
Here, we present a classical x-linked hypohidrotic ectodermal dysplasia with finger clubbing, the association of which is not being reported earlier.
DOI: http://dx.
doi.
org/10.
3126/ajms.
v5i4.
9457
Asian Journal of Medical Sciences 2014 Vol.
5(4); 119-121.
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