Becker’s Nevus Syndrome - Rare entity

Becker’s nevus is a rare non-cancerous hamartoma characterized by hyperpigmentation and hypertrichiosis with ill-defined borders. Becker’s nevus syndrome is an entity in which there is association of Becker’s nevus with few abnormalities like unilateral breast hypoplasia, muscle, skin, and skeletal abnormalities. Here we present a case of 14 year old boy who presented with a large hyper pigmented dark brown patch on his upper back. The patient also had a triangular lesion on his lower back with increased hair growth, which was present since birth. X-Ray spine showed Bifid Spinous process of L4. Histopathological examination of the hyper-pigmented area showed findings which were consistent with Becker’s nevus.