Upper Abdominal Primary Retroperitoneal Cyst with Unusual Urothelial Histogenesis - An Uncommon Presentation Masquerading as a Hepatic Cyst

Background: Benign retroperitoneal cysts are uncommon. There is a paucity of literature on primary upper abdominal retroperitoneal cysts of urothelial histogenesis. We report an uncommon presentation of urothelial cyst clinically mimicking a hepatic cyst. Case presentation: A 21-year old female patient was admitted with intermittent abdominal pain of 9 months duration diagnosed on radiology as a right hepatic cyst. Laparoscopic resection and pathologic examination revealed a primary retroperitoneal cyst with a urothelial histogenesis. This is an unusual clinical presentation of a rare lesion mimicking a hepatic cyst. Conclusion: This case highlights the unusual anatomic location and the rare occurrence of an upper abdominal retroperitoneal urothelial cyst.